Two-Stage Urethroplasty with Buccal Mucosa for Penoscrotal Hypospadias Reconstruction in a Male with a 46,XX Karyotype
نویسندگان
چکیده
We present a case regarding a 32-year old African male with penoscrotal hypospadias, left cryptorchidism and a left inguinal hernia. There were moderate masculinization characteristics. He underwent a Lichtenstein hernia repair with perioperative biopsies of the left inguinal testis and epididymis. Microscopic examination showed a Sertoli-only left testis with Leydig-cell hyperplasia and the left epididymis consisted of ovarian tissue with corpora albicantia and maturing follicles. Endocrinological evaluation showed a sex-determining region Y (SRY) negative 46,XX karyotype. We successfully performed a two-stage urethroplasty with buccal mucosa graft to reconstruct his penoscrotal hypospadias.
منابع مشابه
Buccal mucosa urethroplasty in a reoperative and reconstructive challenge hypospadias: a case report
Buccal mucosa graft is usually used in a second operation. A buccal mucosa graft from the lower lip was used for large fistula reconstruction in one patients. The patient previously had been operated on several times at another center. The use of the buccal mucosa graft for urethral reconstruction in complex urethroplasties is a successful method with a low incidence of complications.
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